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. 2020 May 12;11:888. doi: 10.3389/fimmu.2020.00888

Table 1.

Selected clinical trials of CAR T cells in B-cell acute lymphoblastic leukemia.

Setting Target Product Costimul. domain Generation Vector Population infused Response Durable remission rate CRS (gr.3/4) NTX (gr.3/4) Institute/Company Clinical trial References
B-ALL CD19 Tisagenlecleucel (CTL019, Kymriah®) 4-1BB Second (2nd) Lentiviral 75, R/R pediatric/AYA
B-ALL
(up to 25 yo)
ORR 81%
CR 60%
RFS
80% at 6 mo
59% at 12 mo
47%¥ 13%± UPenn/Novartis ELIANA
NCT02435849 multicenter phase II
(21)
KTE-X19 CD28 Second (2nd) Retroviral 45, R/R adult B-ALL ORR 82%
CR 73%
Median DOR 12.9 mo 29%§ 38%± Kite, Gilead ZUMA-3
NCT02614066
multicenter phase I/II
(30)
24, R/R pediatric/AYA B-ALL CR + CRi rate
64–100%
(related to CART dose)
ongoing remission
25–56% (related to CART dose)
22–75%§ (related to CART dose) 11–36%± (related to CART dose) ZUMA-4
NCT02625480
Multicenter phase I/II
(32)
19-28z-CAR CD28 Second (2nd) Retroviral 53, R/R adult B-ALL CR 83% Unknown 26% 42%± MSKCC/Juno NCT01044069
Phase I
(33)
CD19-28z-CAR CD28 Second (2nd) Retroviral 19, R/R pediatric/AYA
B-ALL
(up to 30 yo)
CR 67% 12-mo LFS 78.8% 28%± 5%¬ NCI NCT01593696
Phase I
(40)
CD4+/CD8+ CD19-BBz-CAR 4-1BB Second (2nd) Lentiviral 45, R/R pediatric/AYA B-ALL MRD CR 89% Unknown 23%± 21%± SCH PLAT-02
NCT02028455
Phase I/II
(41)
CD19-BBz.EGFRt-CAR 4-1BB Second (2nd) Lentiviral 30, R/R adult B-ALL CR 93%
MRD neg 86%
Unknown 23%§ 50%± FHCRC NCT01865617
Phase I/II
(42)
UCART19 4-1BB Allogeneic CAR T cells, gene editing with TALEN Lentiviral 7, R/R pediatric B-ALL CR + CRi 88%
MRD neg 86%
Ongoing remission 28% 15% 0% MDACC, UCL etc./Servier PALL
NCT02808442
Phase I
(43)
13, R/R
Adult B-ALL
Ongoing remission 21% CALM
NCT02746952
Phase I
CD22 CD22-BBz-CAR 4-1BB Second (2nd) Lentiviral 21, R/R pediatric/adult B-ALL CR 73% Median DOR
6 mo
0%± 0%± NIH NCT02315612
Phase I
(44)
¥

, Penn/CHOP grading scale;

§

, NCI 2014 consensus grading scale modified by Lee DW et al. (45);

, MSKCC criteria;

¬

, CTCAE v4.02;

±

, CTCAE v4.03;

CTCAE v5.0.

ALL, acute lymphoblastic leukemia; R/R, relapse/refractory; AYA, adolescent and young adult; ORR, overall response rate; CR, complete remission; CRi, complete remission with incomplete hematologic recovery; MRD, minimal residual disease; mo, months; DOR, duration of response; EFS, event-free survival; RFS, relapse-free survival; LFS, leukemia-free survival; DFS, disease-free survival; NR, not reached; CRS, cytokine release syndrome; NTX, neurotoxicity; UPenn, University of Pennsylvania Hospital; SCH, Seattle Children's Hospital; FHCRC, Fred Hutchinson Cancer Research Center; MSKCC, Memorial Sloane Kettering Cancer Center; NCI, National Cancer Institute; MDACC, MD Anderson Cancer Center; UCL, University College of London.