Table 4. Comparison between diameters of the different portion of aorta in knock-out mouse models of the three different lysosomal storage disease.

MPS: Mucopolysaccharidosis.

	GAA -/- (Pompe) (n = 5)	GLA -/- (Fabry) (n = 5)	NAGLU-/- (MPS IIIB) (n = 5)	p-value
Aortic annulus	1.51 (±0.22)	1.35 (±0.44)	1.36 (±0.09)	0.176
Sinus of Valsalva	1.88 (±0.26)	1.6 (±0.05)	1.46 (±0.11)	0.006*
Sino-tubular junction	1.49 (±0.23)	1.26 (±0.05)	1.16 (±0.08)	0.007*
Ascending aorta	1.61 (±0.17)	1.57 (±0.04)	1.42 (±0.05)	0.037*
Aortic arch	1.51 (±0.24)	1.36 (±0.03)	1.34 (±0.04)	0.149
Descending aorta	1.17 (±0.09)	1.29 (±0.07)	1.18 (±0.04)	0.028*