Table 1.

Hereditary pancreatic cancer syndromes

Disease	Gene	Risk ratio
Hereditary pancreatitis	PRSS1, SPINK1, CFTR, CTRC	60‐87
Hereditary breast and ovarian cancer; HBOC	BRCA1/2	4.1‐5.8
Peutz‐Jeghers syndrome; PJS	STK11/LKB1	132
Familial atypical multiple mole melanoma syndrome; FAMMM	CDKN2A/p16	13‐22
Familial adenomatous polyposis; FAP	APC	4.5
Hereditary non‐polyposis colorectal cancer; HNPCC (Lynch syndrome)	MLH1, MSH2, MSH6, PMS2	8.6