Table 2.
Comparison table of clinical characteristics between Q703K-positive vs. -negative PFAPA patients.
| Q703K+ (n: 21) | Q703K- (n: 129) | P-value | |
|---|---|---|---|
| Median age at onset (years.months) | 2 | 1 | |
| Median duration (days) | 5* | 4.25** | |
| Median interval (days) | 30* | 30** | |
| Sex ratio (M/F) | 2/1 (14/7) | 1/1 (66/63) | 0.2402 |
| Positive familial history | 8/19 | 50/102 | 0.6249 |
| Pharyngitis | 17 | 107/126 | 0.7450 |
| Oral aphthosis | 11 | 65/120 | 1 |
| Adenitis | 16 | 78/128 | 0.2265 |
| Abdominal Pain | 13 | 66/118 | 0.6420 |
| Complete cluster | 7 | 40/116 | 1 |
| Onset after 5 y.o. | 3 | 16/127 | 0.7349 |
| Good response to steroids | 11/11 (100%) | 101/105 (96%) | 1 |
*
data available in 16 patients.
**
data available in 127 patients.