Table 1.
Patient characteristics.
| No. | Age | Sex | Arrhythmia | Antiarrhythmic | Dose/daily | Period between ICD-BCSD (months) | Mutation | Family history of sudden death |
|---|---|---|---|---|---|---|---|---|
| 1 | 4 | F | LQTS-JLNS | NAD | 1 | 5 | KCNQ1 | |
| 2 | 17 | F | CPVT | PRP + FLC | 3 + 100 | 1 | – | 2 siblings |
| 3 | 12 | M | CPVT | PRP + FLC | 3 + 100 | 3 | CASQ2 | |
| 4 | 14 | M | CPVT | PRP + FLC | 3 + 100 | 64 | – | Father |
| 5 | 15 | F | LQTS-7 | PRP | 3 | – | KCNJ2 | 2 siblings |
| 6 | 14 | F | LQTS-7 | PRP | 3 | 10 | KCNJ2 | |
| 7 | 9 | M | LQTS-JLNS | PRP | 3 | 72 | KCNQ1 | Cousin |
| 8 | 13 | M | CPVT | PRP | 3 | 50 | RYR2 | |
| 9 | 15 | F | CPVT | PRP + FLC | 3 + 100 | 48 | – | |
| 10 | 17 | M | CPVT | PRP | 3 | 72 | – | |
| 11 | 7 | M | LQTS-1 + 2 | PRP | 3 | 41 | KCNQ1+ KCNH2 | 1 sibling, mother |
| 12 | 14 | M | LQTS-1 | PRP | 3 | 54 | KCNQ1 | 1 sibling |
| 13 | 10 | F | LQTS-7 | PRP + FLC | 3 + 100 | 50 | – | |
| 14 | 7 | M | LQTS-JLNS | PRP | 3 | 8 | KCNQ1 | |
| 15 | 15 | M | CPVT | PRP + FLC | 3 + 100 | 60 | – | Father, 2 cousins |
F: female M: male LQTS: long-OT syndrome, CPVT: catecholaminergic polymorphic ventricular tachycardia JLNS: Jervell and Lange Nielsen syndrome, LQTS-7: Andersen Tawil syndrome, NAD: nadolol, PRP: propranolol, FLC: flecainide, dose/daily: mg/kg/day for NAD and PRP, mg/m2/day for FLC.