LS |
Leigh syndrome |
MD |
Mitochondrial disorder |
iPSCs |
Induced pluripotent stem cells |
mtDNA |
Mitochondrial DNA |
NSCs |
Neural stem cells |
OXPHOS |
Mitochondrial oxidative phosphorylation system |
DMSO |
Dimethyl sulfoxide |
FCCP |
Carbonyl cyanide p-trifluoromethoxyphenylhydrazone |
RC |
Respiratory chain |
ROS |
Reactive oxygen species |
MELAS |
Mitochondrial myopathy, encephalopathy, lactic acidosis and stroke |
ATP |
Adenosine triphosphate |
ETC |
Electron transfer chain |
rRNA |
Ribosomal ribonucleic acid |
tRNA |
Transfer RNA |
CS |
Citrate synthase |
∆Ψmit |
Mitochondrial membrane potential |
AP |
Action potential |
FRU |
Fluorescence relative units |