Table 1.

Number of individual published mentions of HAE-C1INH and autoimmune disease comorbidity

Autoimmune disease	Number of HAE comorbid mentions
Lupus or lupus-like diseases	52
Systemic lupus erythematosus	30
Lupus (unspecified)	7
Discoid lupus	8
Lupus-like disease	4
Cutaneous lupus	2
Drug-induced lupus	1
Thyroid disease	21
Hypothyroidism	10
Thyroiditis	5
Anti-thyroid antibodies	3
Hashimotos	2
Unspecified	1
Glomerulonephritis	16
Rheumatoid arthritis	11
Crohn’s disease	8
Various autoantibodies	8
Sjogren’s syndrome	7
Celiac disease	7
Psoriasis	3
Antiphospholipid syndrome	3
Autoimmune hemolytic anemia/anemia	3
General/unspecified autoimmune disease	2
Psoriatic arthritis	2
Systemic sclerosis	2
Mixed connective tissue disease	2
Raynauds syndrome	2
Urticarial vasculitis	1
Sicca syndrome	1
Lipodystrophy	1
Alopecia	1
Multiple-sclerosis-like syndrome	1
Ulcerative colitis	1

C1-INH C1 esterase inhibitor, HAE hereditary angioedema