Table 1.
Patient characteristics
| Demographic assessment | No. (%)/median [IQR] |
|---|---|
| Patient age (years) | 16.0 (14.2) |
| Age at Fontan operation (years) | 3.5 (3.3) |
| Duration of Fontan circulation (years) | 10.3 (14.7) |
| Gender | |
| Male | 71 (49.0) |
| Underlying anatomy | |
| Tricuspid atresia | 45 (31.0) |
| Double inlet left ventricle | 21 (14.5) |
| Hypoplastic left heart syndrome | 22 (15.2) |
| Complex transposition of great arteries | 11 (7.6) |
| Unbalanced AVSD | 16 (11.0) |
| RV hypoplasia with PA/IVS | 11 (7.6) |
| Other | 19 (13.1) |
| Predominant ventricular morphology | |
| Left | 95 (66.5) |
| Right | 50 (34.5) |
| Fontan type | |
| Intracardiac lateral tunnel | 22 (15.2) |
| Extracardiac conduit | 109 (75.2) |
| Other | 14 (9.7) |
| Fenestration | |
| Primary | 61 (14.5) |
| Secondary | 6 (4.1) |
| PLE | 12 (8.3) |
AVSD atrioventricular septal defect, RV right ventricle, PA/IVS pulmonary atresia with intact ventricular septum, PLE protein-losing enteropathy