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. Author manuscript; available in PMC: 2020 Jul 23.
Published in final edited form as: J Am Coll Cardiol. 2019 Jul 23;74(3):346–358. doi: 10.1016/j.jacc.2019.05.022

TABLE 2.

Clinical Findings in Patients Categorized by Clinical Phenotype

ARVC
Demographics
2010 Task Force Criteria (11)
Family Patient # Age at Diagnosis, yrs Structural Tissue Repolarization Depolarization Arrhytdmia Family History and Genetics

A 1 13.9 ++ ++ + ++
B 1 15.2 ++ + + ++
C 1 16.8 ++ ++ + + ++
C 2 18.3 + + ++
D 1 15.0 ++ + + ++
E 1 14.5 ++ ++ + +
F 1 22.1 + ++ + + ++
G 1 14.2 ++ + + ++
H 1 20.2 + + ++
H 2 21.8 + ++ + +
I 1 18.4 ++ + + ++
J 1 12.0 ++ + + + ++
K 1 16.5 ++ ++ + ++
L 1 14.3 ++ + + ++
M 1 17.6 ++ + +
N 1 16.1 + + ++

LD ACM
Clinical Features of LD ACM (3)
ECG Arrhythmia Imaging CMR Biopsy Genetics

O 1 13.1
P 1 12.9
Q 1 16.8
R 1 14.6
R 2 13.0
S 1 17.6
T 1 16.9

BiV ACM
2010 Task Force Criteria (11)
Structural Tissue Repolarization Depolarization Arrhythmia Family History and Genetics

U 1 16.0 ++ ++ ++ + + ++
V 1 15.0 ++ ++ + +
V 2 18.8 ++ ++ + +
W 1 4.9 ++ + + + ++
X 1 16.3 ++ ++ + ++ + ++
Y 1 8.9 ++ ++ + ++
Z 1 14.7 ++ ++ ++ + + ++
AA 1 5.6 + + ++
BB 1 11.6 ++ ++ ++ +

Repolarization indicates abnormalities of repolarization on ECG, and depolarization indicates abnormalities of depolarization on ECG.

++

= Major criteria;

+

= minor criteria;

= LD ACM criteria present

CMR = cardiac magnetic resonance; ECG = electrocardiography; other abbreviations as in Table 1.