TABLE 1.

Patient Characteristics (N = 80)

Male, %	42 (53%)
Age at first symptom, yrs	11.0 (6.0-13.0)
Age at diagnosis, yrs	11.0 (7.4-14.0)
Follow-up, yrs	6.4 (2.2-10.0)
Proband	66 (83)
Family history of CPVT	19 (24)
History of cardiac arrest	29 (36)
Positive genetic testing	49 (80)
RyR2	45 (92)
CASQ2	2 (4)
KCNJ2	2 (4)
Antiarrhythmic
β anti-adrenergic blocker	78 (98)
Flecainide	15 (19)
Calcium channel blocker	12 (15)
ICD (n = 49)
Age at implantation, yrs	13.5 (9.3-16.7)
ICD follow up	9.0 (6.0-12.1)
Dual chamber	26 (53)
Left cardiac sympathetic denervation	15 (19)
Deaths	3 (4)

Values are n (%) or median (interquartile range).

CPVT = catechotaminergic polymorphic ventricular tachycardia; ICD = implantable cardioverter defibrillator.