AAV	Adeno-associated virus
AGO	Argonaute
ALS	amyotrophic lateral sclerosis
ATXN2	Ataxin-2
dsRNA	double stranded RNA
EIF2	Eukaryotic initiation factor 2
EWSR1	EWS RNA-binding protein 1
EXO	exosome
EXP	exportin 5
fALS	familial ALS
FMRP	fragile X mental retardation protein
FTLD	frontotemporal lobular dementia
FUS	fused in sarcoma
FUS/TLS	fused in sarcoma/ translocated in liposarcoma
hnRNP	heterogeneous nuclear ribonucleoproteins
HuWtSOD1	human wild-type SOD1
iPSC	induced pluripotent stem cell
LC	low-complexity
MATR3	Matrin-3
miRISC	miRNA-induced silencing complex
miRNA	micro RNA
MN	motor neuron
MV	microvesicle
ND	neurodegenerative disease
NSC-34	Neuroblastoma/spinal cord hybrid
PD	Parkinson’s disease
pre-miRNA	precursor miRNA
pri-miRNA	primary miRNA
PRNP	Prion protein
PY-NLS	PY nuclear localization signal
RACK1	ribosomal receptor for activated C kinase 1
RAN	Ras-related nuclear protein
RBP	RNA-binding protein
RISC	RNA-induced silencing complex
RNP	ribonucleoprotein particle
RRM	RNA recognition motif
sALS	sporadic ALS
SEDI	SOD1 exposed dimer interface
SG	stress granule
SMA	Spinal muscular atrophy
SMN	survival of motor neuron
SNP	subnuclear paraspeckle
SOD1	superoxide dismutase-1
STMN2	Stathmin-2
TA	tibialis anterior
TAF15	TATA-box binding protein associated factor 15
TARDBP	TAR DNA-binding protein
TDP-43	transactive response DNA-binding protein
TIA1	TIA1 cytotoxic granule associated RNA-binding protein
UBQLN2	Ubiquilin-2
UTR	Untranslated region
WT	wild-type