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. 2020 Jun 11;16:495–507. doi: 10.2147/TCRM.S232660

Table 3.

Consensus Classification of Pediatric Behçet Disease

Item Description Value/Item
Recurrent oral aphtosis At least three attacks/year 1
Genital ulceration and aphtosis Typically with scar 1
Skin involvement Necrotic folliculitis, acneiform lesions, erythema nodosum 1
Ocular involvement Anterior uveitis, posterior uveitis, retinal vasculitis 1
Neurological signs With the exception of isolated headaches 1
Vascular signs Venous thrombosis, arterial thrombosis, arterial aneurysm 1

Note: Three of six items are required to classify a patient as having pediatric Behçet disease. Data from Kone-Paut et al.49