Table 1.
Demographic Profile of NF1 and NF2 Patients
| NF1 (n = 162) | NF2 (n = 22) | |
|---|---|---|
| AGE (mean ± SD) | 33 ± 13.5 | 40 ± 15.2 |
| Female/male | 92 (57%)/70 (43%) | 13 (59%)/9 (41%) |
| Marital statusa | ||
| Single | 101 (65%) | 13 (59%) |
| Married/common law | 47 (30%) | 7 (31%) |
| Divorce/separated | 4 (2.5%) | 1 (5%) |
| Other (living with partner, widow) | 4 (2.5%) | 1 ((5%) |
| Highest educationb | ||
| Some or completed primary | 5 (3%) | 1 (4%) |
| Some or completed secondary | 34 (22%) | 2 (9%) |
| Some or completed trade or community program | 57 (37%) | 9 (41%) |
| Some or completed university | 58 (38%) | 10 (46%) |
| Work statusc | ||
| Employed | 75 (49%) | 10 (50%) |
| Unemployed | 10 (6%) | 4 (20%) |
| Disability | 24 (16%) | 5 (25%) |
| Student | 35 (23%) | 1 (5%) |
| Other | 9 (6%) | 0 (0%) |
| History of MPNST | 14 (9%) | NA |
| Optic glioma | 25 (15%) | NA |
| Known plexiform neurofibroma | 63 (39%) | NA |
| Ablon’s index (median, range) | 2 (1–3) | NA |
| Hearing | ||
| Normal | NA | 8 (36%) |
| Mild to moderate hearing loss | NA | 7 (32%) |
| Severe or profound hearing loss | NA | 7 (32%) |
| Facial nerve scale | ||
| Grade 1 | NA | 14 (63%) |
| Grades 2 and 3 | NA | 5 (23%) |
| Grades 5 and 6 | NA | 3 (14%) |
MPNST, malignant peripheral nerve sheath tumor.
a156 patients with NF1 and 22 with NF2 completed the marital status question.
b154 patients with NF1 and 22 with NF2 completed the education question.
c153 patients with NF1 and 20 with NF2 completed the employment question.