TABLE 1.
Demographics of the Johns Hopkins and Radboudumc cohorts
Disease group | Number of subjects | Male/female | Mean age, years (range) | BMI, kg/m2 (range) | Duration of symptoms, months (range) |
---|---|---|---|---|---|
Johns Hopkins | |||||
IBM | 25 | 12/13 | 65.1 (52–80) | 25.5 (19.1–34.4) | 116.9 (30–360) |
PM/DM | 21 | 5/16 | 67.0 (51–87) | 26.0 (17.3–39.5) | 66.6* (7–216) |
Healthy controls | 25 | 9/16 | 65.9 (51–80) | 26.8 (19.7–36.8) | Not available |
Radboudumc | |||||
IBM | 16 | 9/7 | 70.5 (54–84) | 24.9 (19.6–33.6) | 67.2 (12–228) |
PM/DM | 16 | 6/10 | 64.8 (54–76) | 26.9 (21.3–36.1) | 35.2 (1–276) |
Neuromuscular controls | 11 | 6/5 | 65.2 (51–75) | 27.0 (22.6–41.4) | 50.2 (6–162) |
Healthy controls | 63 | 28/35 | 63.4* (50–82) | 25.1 (18.8–34.9) | Not available |
BMI, body mass index; DM, dermatomyositis; IBM, inclusion body myositis; PM, polymyositis.
Neuromuscular controls: myopathies (n = 5), motor neuron diseases (n = 4), polyneuropathy (n = 1) and Lambert‐Eaton myasthenic syndrome (n = 1).
P < .05 vs IBM.