Table 2.
Summary of studies on the prevalence of primary Sjögren’s syndrome in the adult population (≥ 18 years old) using the 2002 American-European Consensus Group (AECG) criteria.
| AuthorRef | Year | Country | Source of cases | Study design | Population size (N) | pSS cases (N) | Female/male (N) | Prevalence % Prevalence rate (95% CI)/100,000 |
|---|---|---|---|---|---|---|---|---|
| Maciel et al3 | 2015 | USA (Olmsted County, Minnesota) | Medical record linkage system | Population based | 113,306 | 23 | NS |
0.02% 22 (1.3–3.1) |
| Valim et al.5 | 2013 | Brazil (Vitoria) |
Questionnaire Clinical examination |
Cross-sectional population survey | 1,205 | 2 | NS |
0.06% 60.82 (43.69–77.94) |
| Anagnostopoulos et al.10 | 2010 | Greece (Prefecture) |
Questionnaire Clinical examination |
Cross-sectional population survey | 1,705 | 4 | NS |
0.23% 234.60 (4.70–464.51) |
| Birlik et al.11 | 2009 | Turkey (Balcova, Narlidere) |
Questionnaire Clinical examination |
Population survey | 2,887 | 6 | 6/0 |
0.21% 207.83 (41.53–374.12) |
| Alamanos et al.14 | 2006 | Greece (north-west Greece) |
Personal registry physicians Medical record search |
Population based | 488,435 | 422 | 402/20 |
0.09% 86.40 (78.16–94.64) |
| Kabasakala et al.15 | 2006 | Turkey (Bornova) |
Questionnaire Clinical examination |
Cross-sectional population survey | 831 | 6 | NS |
0.72% 722.02 (144.29–1,299.75) |
| Trontzas et al.16 | 2005 | Greece |
Questionnaire Clinical examination |
Population survey | 8,470 | 13 | NS |
0.15% 0.08% ages 44–64 years 0.40% ages > 65 years 148.74 (67.89–229.60) |
aThe study was only conducted in female population.