Table 2.
Summary of the nutritional treatment.
| Total Energy (kcal/d) | Total Protein (g/day) | Intact Protein (g/day) | Valine Intake (mg/day) |
|||||||||
|---|---|---|---|---|---|---|---|---|---|---|---|---|
| Patient | Age (years) | Weight (kg) | Baseline | Last Rx | Baseline | Last Rx | Baseline | Last Rx | Decrease (%) | Baseline | Last Rx | Decrease (%) |
| 1 | 13.0 | 39 | 1250 | 1055 | 50 | 44.3 | 50 | 11.3 | 77 | 2254 | 653 | 71 |
| 2 | 14.5 | 44 | 1250 | 1055 | 50 | 44.3 | 50 | 11.3 | 77 | 2254 | 653 | 71 |
| 3 | 6.3 | 13 | 1630 | 2117 | 30 | 19.5 | 30 | 19.5 | 35 | 1795 | 1167 | 35 |
| 4 | 13.8 | 45 | 1725 | 1190 | 65 | 37.0 | 65 | 37.0 | 43 | NA | NA | NA |
| 5 | 3.8 | 15 | 932 | 880 | 39 | 20.1 | 39 | 9.6 | 75 | 2452 | 605 | 75 |