| SCA | Spinocerebellar ataxia |
| ER | Endoplasmic Reticulum |
| ERAD | Endoplasmic Reticulum-associated degradation |
| EDEM1 | ER degradation-enhancing α mannosidase-like 1 protein |
| BiP | Immunoglobulin binding protein |
| WT | wildtype |
| RFP | Red fluorescent protein |
| Endo H | Endoglycosidase H |
| PNGase F | Peptide N glycosidase F |
| TM | Transmembrane |
| SGFP2 | Strongly enhanced green fluorescent protein 2 |
| RNAi | RNA interference |
| CHX | Cycloheximide |
| KIF | Kifunensine |
| Clq | Chloroquine |