Table 5.
Review of pediatric pulmonary hypertension registries.
| Author | Publication Year | N | Incidence (N per Million Children) | Prevalance (N per Milion Children) | Diagnosis (%) | Symptoms (%) | Down Syndrome (%) | ||||||||
|---|---|---|---|---|---|---|---|---|---|---|---|---|---|---|---|
| IPAH | PAH-CHD | IPAH | PAH-CHD | IPAH | PAH-CHD | Other PAH | Fatigue | Excercise Dyspnea | Dyspnea | Chest pain | Syncope | ||||
| Moledina [29] | 2010 | 64 | 0.48 | 2.1 | IPAH only | 31 | 31 | 75 | 31 | 4.7 | |||||
| Fraisse [12] | 2010 | 50 | 2.2 | 60 | 24 | 16 | 72 | 76 | 7 | 11 | |||||
| van Loon [11] | 2011 | 154 | 0.7 | 2.2 | 4.4 | 15.6 | 23 | 72 | 5 | 70 | 43 | 1 | 7 | 18 | |
| Barst [4] | 2012 | 216 | 56 | 36 | 8 | 24 | 46 | 9 | 5 | 24 | |||||
| del Cerro [22] | 2014 | 142 | 0.49 | 2.9 | 21 | 74 | 5 | 76 | 6.2 | 9.3 | 17 | ||||
| Kwiatkowska | 2020 | 80 | 3.6 | 7.8 | 31 | 67 | 2 | 90 | 70 | 20 | 1.25 | 1.25 | 30 | ||
IPAH, idiopathic pulmonary arterial hypertension; PAH-CHD, pulmonary arterial hypertension associated with congenital heart disease