Figure 1.

Category shifts among patients with ALS at follow-up. Proportions of patients with ALS (n=28) with no (green), mild (blue) or severe (red and pink) cognitive and/or behavioural impairment at baseline (upper bar) and follow-up (lower bar). Severe behavioural impairment is compatible with the behavioural variant of frontotemporal dementia. Ten patients shifted towards a more severe category: six from ‘no’ to ‘mild’ cognitive impairment, one from ‘no’ to ‘mild’ behavioural impairment, two from ‘no’ to ‘severe’ behavioural impairment and one from ‘no’ to ‘mild’ cognitive impairment and ‘severe’ behavioural impairment. ALS, amyotrophic lateral sclerosis.