Table 1.
Patient | Emergent (24-48 Hours of Diagnosis When Adequate Resources) | Urgent (Within 1-2 Weeks When Adequate Resources) | High Priority Elective (>2 Weeks When Adequate Resources) |
---|---|---|---|
Neonate | Note: Timing for categories will depend on resources available, institutional protocols, and other pending cases | ||
Shunts: right → left | |||
TAPVC/cor triatriatum | Obstructed | Increasing gradient | |
TGA | <1 week if IVS | 2-4 weeks if VSD | |
Truncus arteriosus | If stable | ||
Tetralogy of Fallot | Spelling/deep cyanosis | Symptomatic | |
Regurgitant lesions | |||
Ebstein anomaly | Refractory medical management | ||
Obstructive lesions | |||
Coarctation | Shock unable to stabilize on PGE | If able to stabilize on PGE | |
Critical aortic stenosis | Shock unable to stabilize on PGE | If able to stabilize on PGE | |
PGE-dependent pulmonary blood flow | |||
PA/IVS | If PDA stent not available | ||
PGE-dependent systemic blood flow | |||
HLHS | Intact, restrictive atrial septum if BAS not available | Case and surgeon dependent | Case and surgeon dependent |
Other | |||
Shunt | Shunt thrombosis | Shunt stenosis | |
Arrhythmias | Symptomatic congenital heart block unable to medically manage/externally pace | ||
ALCAPA | Once medically stabilized | ||
Infant | |||
Shunts: left → right | |||
VSD | Symptomatic CHF on medical management | Failure to thrive | |
Shunts: right → left | |||
Tetralogy of Fallot | Symptomatic (spells, cyanosis) on medical management | ||
Regurgitant lesions | |||
AVSD | Tri21 with pulmonary overcirculation, consider age of patient to optimize repair, significant regurgitation unable to manage medically | ||
Ebstein anomaly | Increasing right-sided heart failure on medical management | ||
Mitral regurgitation | Symptomatic CHF on medical management | ||
Aortic regurgitation | Acute, hemodynamically unstable | Enlarging LV, decreasing LVEF, symptoms | |
Obstructive lesions | |||
Valve prosthesis | Thrombosed prosthesis | ||
AS/LVOTO | Decreasing LVEF, symptoms | ||
RVOTO | Decreased RV function | ||
Other | |||
Shunt | Shunt thrombosis | Shunt stenosis | |
DCM/HF | CHF failing medical management | Failure to thrive | |
BDCPA candidate | Increasing cyanosis with current shunt, shunt stenosis |
Abbreviations: ALCAPA, anomalous left coronary artery from the pulmonary artery; AS, aortic stenosis; AVSD, atrioventricular septal defect; BDCPA, bidirectional cavopulmonary anastomosis ; CHF, congestive heart failure; DCM/HF, dilated cardiomyopathy/heart failure; HLHS, hypoplastic left heart syndrome; LV, left ventricle; LVEF, left ventricular ejection fraction; LVOTO, left ventricular outflow tract obstruction; PA/IVS, pulmonary atresia with intact ventricular septum; PGE, prostaglandin E; RV, right ventricle; RVOTO, right ventricular outflow tract obstruction; TAPVC, total anomalous pulmonary venous connection; TGA, transposition of great artery; VSD, ventricular septal defect.
a Reproduced from Stephens et al.8