Table 1. Patients characteristics.
Parameter | Total (No. = 8) |
---|---|
Male, No. (%) | 5 (63) |
Age, years (median, IQR range) | 16 (9–26) |
Surgical history FESS, No. (%) | 2 (25) |
Genotype | |
ΔF508/S1251N, No. (%) | 7 (88) |
A455E/S1251N, No. (%) | 1 (12) |
Other medication beside ivacaftor | |
Nasal steroids, No. (%) | 6 (75) |
Nasal saline irrigation, No. (%) | 2 (25) |
Systemic antibiotics, No. (%) | 7 (88) |
Systemic steroids, No. (%) | 2 (25) |
Abbreviations: No.: number of patients, FESS: functional endoscopic sinus surgery, IQR: interquartile range