Table 1.
Clinical characteristics of MuSK-MG patients at the time of blood draw (N=31).
Patient NO. | Age(Yr) | Gender | Onset-age(Yr) | Disease duration(mo) | Race | ThymX | MGFA | MMT | Treatment (daily dose) |
---|---|---|---|---|---|---|---|---|---|
1 | 23 | Female | 22 | 13 | B | 2B | 3 | Pred 20mg | |
2 | 48 | Female | 36 | 150 | W | I | 1 | MMF 2000mg | |
3 | 60 | Female | 45 | 186 | B | 2B | 3 | Pred 10mg+MMF2000mg | |
4 | 23 | Female | 10 | 154 | B | 2A | 5 | MMF 1500mg | |
5 | 46 | Female | 45 | 14 | B | I | 3 | Pred 20mg | |
6 | 29 | Female | 20 | 109 | B | 0 | 0 | None | |
7 | 67 | Female | 49 | 218 | W | 2A | 3 | MMF 2000mg | |
8 | 56 | Female | 42 | 161 | W | Yes | 2B | 2 | None |
9 | 65 | Female | 53 | 139 | W | Yes | 1 | 3 | Pred 1.25mg +MMF 2000mg |
10 | 63 | Female | 51 | 146 | W | 3B | 23 | Pred 5mg +AZA 150mg | |
11 | 64 | Female | 30 | 402 | W | Yes | 2B | 9 | MMF 500mg |
12 | 31 | Female | 26 | 58 | B | Yes | 3B | 20 | Plasma exchange |
13 | 47 | Female | 34 | 157 | B | 2B | 3 | Pred 7.5mg + MMF 2000mg | |
14 | 23 | Female | 21 | 20 | B | 2A | 2 | Pred 30mg + MMF 2000mg | |
15 | 51 | Male | 43 | 94 | B | 1 | 1 | AZA 75mg | |
16 | 26 | Female | 17 | 112 | Mixed | Yes | 2B | 2 | Pred 20mg + MMF 2500mg |
17 | 58 | Female | 43 | 187 | B | Yes | 2B | 5 | MMF 2000mg |
18 | 40 | Female | 34 | 78 | B | 2B | 5 | MMF 2000mg | |
19 | 31 | Female | 20 | 138 | W | 0 | 0 | None | |
20 | 44 | Female | 29 | 185 | B | 2B | 6 | Pred 10mg | |
21 | 48 | Female | 32 | 184 | B | 2B | 7 | Pred 15mg | |
22 | 66 | Female | 48 | 215 | W | 2B | 4 | Pred 1mg | |
23 | 35 | Female | 33 | 28 | B | 3B | 26 | Mestinon 180mg + pred 30mg | |
24 | 45 | Male | 37 | 104 | Unknown | 2B | 9 | None | |
25 | 28 | Female | 4 | 288 | W | 2A | 7 | Pred 7.5mg + MMF 3000mg | |
26 | 48 | Female | 9 | 476 | W | 3B | 31 | Plasma exchange | |
27 | 56 | Female | 36 | 235 | B | 2A | 21 | None | |
28 | 58 | Female | 44 | 173 | B | 3B | 27 | Pred 20mg | |
29 | 53 | Male | 41 | 146 | B | Yes | 1 | 3 | Pred 5mg |
30 | 28 | Female | 27 | 16 | W | 2B | 17 | MMF 2000mg | |
31 | 25 | Female | 5 | 239 | B | Yes | 3A | 4 | Pred 3.8mg |
Abbreviations: AZA = azathioprine; B = black; d = day; F = female; mg = milligrams; M= male; MGFA = Myasthenia Gravis Foundation of America; MM = minimal manifestations; MMF = mycophenolate mofetil; MMT = myasthenia gravis manual muscle testing score at time of blood draw; Mo = months; Pred = predinison; ThymX= thymectomy; W = white; Yr = years.