Table 2. Cryopyrin-Associated Periodic Syndrome (CAPS) .

FCAS: familial cold autoinflammatory syndrome, MWS: Muckle–Wells syndrome, CINCA: chronic infantile neurological cutaneous articular syndrome, AD: autosomal dominant, AA: amyloid A [24]

FCAS	MWS	CINCA
Inheritance
AD	AD	AD, sporadic
Main clinical features
Cold-induced:	Fever	Fever
-Fever	Urticarial rash	Urticarial rash
-Rash	Conjuctivitis	Conjuctivitis
-Conjunctivitis	Arthralgia	Visual and intellectual damage
-Arthralgia	Sensorineural deafness	Sensorineural deafness
	AA amyloidosis (in 25% of patients) leading to renal failure	Progressive chronic meningitis
		Destructive arthritis
		AA amyloidosis leading to renal failure