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. Author manuscript; available in PMC: 2020 Aug 3.
Published in final edited form as: Circulation. 2012 Mar 2;125(17):2165–2170. doi: 10.1161/CIRCULATIONAHA.112.092924

Table 2.

Pediatric PHVD Classification

1. Prenatal or developmental PHVD
2. Perinatal pulmonary vascular maladaptation
3. Cardiovascular disease
4. Bronchopulmonary dysplasia
5. Isolated PHVD
6. Multifactorial PHVD in congenital malformation syndromes
7. Lung disease
8. Thromboembolic disease
9. Hypobaric hypoxia exposure
10. PHVD with systemic disorders

PHVD indicates pulmonary hypertensive vascular disease.