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. 2019 Nov 13;77(17):3423–3439. doi: 10.1007/s00018-019-03359-z

Fig. 1.

Fig. 1

Pathway of lysine–tryptophan catabolism. Mitochondrial enzymatic defects in tryptophan, lysine, and hydroxylysine degradation pathway found in alpha-ketoadipic aciduria, GA1, and GA3 diseases. KA ketoadipic aciduria, DHTKD1 dehydrogenase E1 and transketolase domain containing 1; [72]; GCDH glutaryl-CoA dehydrogenase, SUGCT succinate hydroxymethylglutarate CoA-transferase