Fig. 1.
Pathway of lysine–tryptophan catabolism. Mitochondrial enzymatic defects in tryptophan, lysine, and hydroxylysine degradation pathway found in alpha-ketoadipic aciduria, GA1, and GA3 diseases. KA ketoadipic aciduria, DHTKD1 dehydrogenase E1 and transketolase domain containing 1; [72]; GCDH glutaryl-CoA dehydrogenase, SUGCT succinate hydroxymethylglutarate CoA-transferase