Table 1:

Baseline Characteristics of the Subjects

Median (range) or Number (%)
Characteristics	All Subjects (n = 40)
Demographic
Age at enrollment (years)	11 (3–34)
Male	30 (75%)
Caucasian	32 (80%)
BMI	17.16 (12.77–35.36)
Age at Fontan operation (years)	2 (1–16)
Years from Fontan (years)	6.50 (1–28)
Primary congenital defect
HLHS	16 (40%)
TA	7 (17.5%)
DORV	10 (25%)
Other	7 (17.5%)
Systemic ventricle anatomy
Morphologically left	14 (35%)
Morphologically right	21 (52.5%)
Morphologically both	5 (12.5%)
Fontan Surgery
Extracardiac conduit	10 (25%)
■ Age at enrollment (years)	11 (5–34)
■ Years from Fontan (years)	5.5 (1–28)
Extracardiac pericardial	15 (37.5%)
■ Age at enrollment (years)	6 (3–12)
■ Years from Fontan (years)	3 (1–9)
Lateral tunnel	15 (37.5%)
■ Age at enrollment (years)	14 (7–22)
■ Years from Fontan (years)	12 (4–20)

BMI: body mass index; DORV: double outlet right ventricle; HLHS: hypoplastic left heart syndrome; TA: tricuspid atresia