Table 3.
Mean values of dark-adapted electroretinogram (ERG), light-adapted ERG, and 30-Hz flicker ERG (F-ERG) responses assessed in control subjects (C) and in patients with Joubert syndrome with (JS-RD group) or without (JS-NRD group) retinal dystrophy
| Dark-adapted ERG | Light-adapted ERG | F-ERG | |||||||
|---|---|---|---|---|---|---|---|---|---|
| a-wave | b-wave | a-wave | b-wave | A (log µV) | |||||
| IT (log ms) | A (log µV) | IT (log ms) | A (log µV) | IT (log ms) | A (log µV) | IT (log ms) | A (log µV) | ||
| C (N = 25) | |||||||||
| Mean | 13.271 | 46.125 | 28.875 | 71.542 | 11.042 | 12.933 | 28.813 | 29.355 | 34.063 |
| SD | 0.766 | 2.597 | 2.849 | 4.688 | 1.444 | 2.083 | 1.131 | 3.852 | 2.288 |
| JS-RD (N = 16) | |||||||||
| Mean | 15.613 | 26.081 | 41.738 | 38.110 | 13.069 | 8.819 | 34.047 | 16.469 | 15.806 |
| SD | 3.111 | 10.369 | 10.333 | 20.099 | 2.786 | 4.486 | 8.827 | 10.498 | 9.138 |
| AV vs C | |||||||||
| f(1,40) | 13.101 | 86.142 | 35.053 | 64.561 | 9.392 | 16.332 | 8.692 | 31.444 | 92.022 |
| p | < 0.001 | < 0.001 | < 0.001 | < 0.001 | < 0.001 | < 0.001 | < 0.001 | < 0.001 | < 0.001 |
| JS-NRD (N = 8) | |||||||||
| Mean | 15.275 | 29.325 | 37.938 | 43.066 | 15.000 | 8.625 | 29.188 | 18.425 | 20.613 |
| SD | 2.647 | 14.336 | 5.421 | 18.930 | 4.520 | 4.211 | 1.624 | 5.129 | 14.102 |
| AV vs C | |||||||||
| f(1,32) | 11.951 | 33.133 | 45.644 | 50.182 | 15.252 | 15.283 | 0.543 | 41.543 | 22.392 |
| p | 0.002 | < 0.001 | < 0.001 | < 0.001 | < 0.001 | < 0.001 | 0.469 | < 0.001 | < 0.001 |
| AV vs JS-RD | |||||||||
| f(1,23) | 0.073 | 0.402 | 0.944 | 0.345 | 1.692 | 0.954 | 2.330 | 0.241 | 1.032 |
| p | 0.795 | 0.531 | 0.343 | 0.567 | 0.208 | 0.341 | 0.141 | 0.626 | 0.322 |
ANOVA statistical evaluation by one-way analysis of variance between groups. p values less than 0.01 were considered as statistically significant (in bold)
N number of eyes, SD standard deviation, IT implicit time, A amplitude, ms milliseconds, µV microvolt