| Differential Diagnosis |
Pertinent Positives |
Pertinent Negatives |
| Cutis aplasia |
Present in early infancy as focal erosion of scalp [8] |
Smoother papyraceous surface; healing with atrophy and scarring [8] |
| Solitary mastocytomas |
Present in early infancy [8] |
Pink, nodular surface; favors distal extremities [8] |
| Congenital triangular alopecia |
Congenital; localized to frontotemporal scalp [8] |
Triangular temporal hair loss; size of lesion unchanged through lifespan [8] |
| Syringocystadenomatous papilliferus (SCAP) |
Association with nevus sebaceous; yellow papules; lesions increase in size at puberty [9] |
Presents in association with apocrine adenoma, trichoblastoma, and eccrine poroma [9] |
| Giant congenital nevus |
Present in early infancy [8] |
Tan color; favors extremities and trunk; hairy lesion [8] |
| Schimmelpenning-Feuerstein-Mims syndrome |
Epidermal nevus present in early infancy [8] |
Seizures and intellectual disability; multisystem manifestations [8] |
