Fig. 1.

Illustrations of normal a heart circulation and a Fontan circulation in two girls. Left, a normal heart with pulmonary and arterial circulation in parallel. Right, a girl with a total cavo-pulmonary connection with an extracardiac conduit (yellow), the Fontan circulation, where the pulmonary and arterial circulations are serial and bypass the right ventricle. The inferior vena cava is enlarged because of increased central venous pressure. Illustrations created by Michael Bjaanes in collaboration with the Department of Pediatric Cardiology at Oslo University Hospital