| CoQ10 | Co-enzyme Q10 |
| ERT | enzyme replacement therapy |
| LSD | lysosomal storage diseases |
| MRC | mitochondrial respiratory chain |
| NO | Nitric oxide |
| iNOS | inducible nitric oxide synthase |
| NPC | Niemann Pick C |
| OS | oxidative stress |
| ROS | redox oxidative stress |
| SCMAS | Subunit c of mitochondrial ATP synthase |
| SOD | Superoxide dismutase |
| V-ATPase | Lysosomal ATPase |
| TLR | Toll-like receptor |