Skip to main content
. 2020 Aug 11;9(8):2596. doi: 10.3390/jcm9082596
CoQ10 Co-enzyme Q10
ERT enzyme replacement therapy
LSD lysosomal storage diseases
MRC mitochondrial respiratory chain
NO Nitric oxide
iNOS inducible nitric oxide synthase
NPC Niemann Pick C
OS oxidative stress
ROS redox oxidative stress
SCMAS Subunit c of mitochondrial ATP synthase
SOD Superoxide dismutase
V-ATPase Lysosomal ATPase
TLR Toll-like receptor