ALCAR—l-Acetyl-carnitine	ARE—Antioxidant response element
dPUFAs—Deuterated PUFAs	DRG—Dorsal root ganglia
ER - Endoplasmic Reticulum	FARS—Friedreich Ataxia Rating Scale
FRDA—Friedreich’s ataxia	GPX4—Glutathione peroxidase 4
ICARS—International Cooperative Ataxia Rating Scale	ISC—Iron-sulphur clusters
KEAP1—Kelch-like ECH-associated protein 1	KIKO—Knock-in/knock out
mFARS—Modified Friedreich Ataxia Rating Scale	NRF2—Nuclear factor erythroid 2-related factor 2
NRFs—Nuclear respiratory factors	OXPHOS—Oxidative phosphorylation
PGC1-α—Peroxisome proliferator-activated receptor gamma coactivator 1-alpha	PPARγ—Peroxisome proliferator-activated receptor gamma
PPARs—Peroxisome proliferator-activated receptors	PUFAs—Polyunsaturated fatty acids
P-VEPs—Visual evoked potentials	ROS—Reactive oxygen species
SARA—Scale of Assessment and Rating of Ataxia	SIRT1—NAD-dependent deacetylase sirtuin-1
SOD2—Superoxide dismutase 2	SREBP1—Sterol-responsive element-binding protein 1
SWJs—Square-wave jerks	TZDs—Thiazolidinediones