Table 1.
Participant | Age | Gender | Diagnosis | Years since diagnosis | Motor impairment | Intelligibility deficit in monologue (0–9 scale) |
---|---|---|---|---|---|---|
1 | 45 | M | FRDA | 17 | moderate | 7.5 mild |
2 | 32 | F | FRDA | 22 | severe | 2 severe |
3 | 36 | F | FRDA | 25 | severe | 2 severe |
4 | 52 | M | FRDA | 14 | moderate | 6.5 mild - moderate |
5 | 40 | M | FRDA | 24 | severe | NA |
6 | 59 | F | FRDA | 46 | moderate | 4 moderate |
7 | 23 | F | FRDA | 13 | moderate | 7.5 mild |
8 | 54 | F | FRDA | 10 | moderate | 8.5 normal |
9 | 75 | F | FRDA | 17 | severe | 7.5 mild |
10 | 31 | F | FRDA | 22 | moderate | 7 mild - moderate |
11 | 40 | M | FRDA | 21 | severe | 9 normal |
12 | 32 | M | FRDA | 21 | severe | 5.5 moderate |
13 | 25 | M | FRDA | 10 | moderate | 3.5 moderate - severe |
14 | 48 | F | FRDA | 30 | moderate | 5 moderate |
15 | 29 | M | FRDA | 21 | severe | 5.5 moderate |
16 | 19 | M | FRDA | 9 | moderate | 5 moderate |
17 | 31 | F | FRDA | 22 | severe | 4.5 moderate |
18 | 71 | F | FRDA | 12 | moderate | 7 mild moderate |
19 | 49 | M | SPG7 | 5 | moderate | 5.5 moderate |
20 | 70 | M | ICA | 12 | moderate | 6.5 mild - moderate |
21 | 73 | M | SCA6 | 19 | moderate | 4 moderate |
Summary: |
Mean: 44.5 SD: 17.3 |
M: n = 11 F: n = 10 |
Mean: 18.7 SD: 8.9 |
Moderate n = 13 Severe n = 8 |
Mean: 5.5 SD: 2.1 |
M male, F female; FRDA Friedreich’s Ataxia, SCA6 Spino-Cerebellar Ataxia Type 6, ICA Idiopathic Cerebella Ataxia; SPG7 Spastic Paraplegia 7