Table 4.
Diet therapy over time, from 2004 to 2019. In 2015 the patient started with the ketogenic diet (KD). BMI = body mass index.
| Year | Age | Height | Weight | BMI | Diet basic | Meals | Energy | Carb | Proteins | Fat | Cornstarch | Notes | |
|---|---|---|---|---|---|---|---|---|---|---|---|---|---|
| 2009/04 | 5 years | Diet therapy | Classic diet GSD IIIa | 5 meals (interval 3 h) -all meals energy and nutritional equal- + 1 night meal 20 g oatmeal + 200 ml Prosure drink | 1370 kcal | 178.0 g (53%) | 78.1 g (23%) | 35.0 g (23%) | |||||
| 2009/11 | Food diary analysis | 8-10 meals (interval 1–3 h) + 1 night meal 20 g oatmeal + 100 ml Prosure drink | 1580 kcal | 244.9 g (62%) | 79.0 g (20%) | 31.6% (18%) | 20 g oatmeal + 100 ml Prosure at 23:00 | Lot of simple sugars | |||||
| 2010/03 | 6 years | Diet therapy | Classic diet GSD IIIa | 5 meals (interval 3 h) -all meals energy and nutritional equal- + 1 night meal 20 g oatmeal + 200 ml Prosure drink | 1500 kcal | 200.0 g (53%) | 86.2 g (23%) | 38.3 g (23%) | |||||
| 2010/11 | Food diary analysis | 8–10 meals (interval 1–3 h) + 40 g cornstarch at 23:00 | 1842 kcal | 303 g (66%) | 50.6 g (11%) | 47.1 g (23%) | 30 g corn starch + 100 ml Supportan dink at 23:00 | Lot of simple sugars. Supplement Supportan drink 200 ml / day | |||||
| 2011/04 | 7 years | 117.1 cm (5p) | 23.4 kg (30p) | 17 (66p) | Diet therapy | Classic diet GSD IIIa | 5 meals (interval 3 h) -all meals energy and nutritional equal- + 1 night meal 30 g corn starch | 1600 kcal | 210 g (53%) | 92 g (23%) | 41 g (23%) | ||
| 2011/11 | Food diary analysis | 8–10 meals (interval 1–3 h) + 40 g corn starch at 23:00 | 1932 kcal | 313.9 g (65%) | 72.4 g (15%) | 43.0 g (20%) | 30 g cornstarch + 100 ml Supported dink at 23:00 | Lot of simple sugars. Supplement Supportan drink 200 ml / day | |||||
| 2012–2013 | 8–9 years | 118.3 cm (3p) | 23.7 kg (23p) | 16.9 (66p) | no data | ||||||||
| 2014/4 | 10 years | 129.9 cm (3p) | 34.15 kg (46p) | 20.4 (87p) | Food diary analysis | 8–10 meals (interval 1–3 h) + 40 g corn starch at 23:00 | 2408 kcal | 363 g (61%) | 97.0 g (15%) | 59.1 g 22%) | 40 g corn starch + 100 ml Fresubin protein drink at 23:00 | Lot of simple sugars. Supplement Supportan drink 200 ml / day | |
| 2014/04 | Diet therapy | Classic diet GSD IIIa | 5 meals (interval 3 h) -all meals energy and nutritional equal- + 1 night meal 30 g corn starch | 1800 kcal | 178.0 g (53%) | 78.1 g (23%) | 35.0 g (23%) | ||||||
| 2015/5 | 11 years | 135 cm | 39.1 kg | 21.4 (91p) | Food diary analysis | 11–14 meals (interval 1–1.5 h) + 40 g corn starch at 23:00 | 2549 kcal | 347 g (55%) | 114.0 g (18%) | 75.3 g (27%) | 40 g corn starch at 23:00 + 100 ml Fresubin protein drink | Lot of simple sugars. Supplement Supportan drink 200 ml / day + Fresubin Energy 200 ml / day | |
| 2015/05 | 11 years | 135 cm | 39.1 kg | 21.4 (91p) | Diet therapy | Transition to ketogenic diet | 6 meals (interval 3.5 h), last meal at 23:00 in the ratio 4: 1 | 2000 kcal | 11.7 g (2%) | 61.0 g (11%) | 204.2 g (87%) | Ketocal 4: 1 for night meal | |
| 2016/6 | 12 years | 138.5 cm (3p) | 36.4 kg (20p)) | 19.0 (59p) | Food diary analysis | Ketogenic diet 2.5: 1 | 6 meals (interval 3.5 h), last meal at 23:00 in a ratio of 4: 1 | 2123 kcal | 11.7 g (2%) | 61.0 g (11%) | 204, 2 g (87%) | Ketocal 4: 1 for a night meal | Follows the diet |
| 2016/09 | Diet therapy | Ketogenic diet 2.5: 1 | 6 meals (interval 3.5 h) last meal at 23:00 in a ratio of 4: 1 | 2000 kcal | 10.0 g (2%) | 60,0 g (12%) | 190,0 g (86%) | Ketocal 4: 1, for a night meal | |||||
| 2018/9 | 14 | 145,3 cm (1p) | 43.3 kg (12p) | 20.4 (59p) | Food diary analysis | Ketogenic diet 2.8: 1 | 6 meals (interval 3.5 h) last meal at 23:00 in a ratio of 4: 1 | 1800 kcal | 10.0 g (2%) | 51.9 g (12%) | 175.0 g (86%) | Ketocal 4: 1 for night meal | Follows the diet |
| 2018/09 | Diet therapy | Ketogenic diet 2.5: 1 | 6 meals (interval 3.5 h) last meal at 23:00 in a ratio of 4: 1 | 2000 kcal | 10.0 g (2%) | 60.0 g (12%) | 190 0g (86%) | Ketocal 4: 1 for night meal | |||||
| 2019/6 | 15 years | 147.7 cm (1p) | 43.8 kg (5p) | 19.8 (44p) | Food diary analysis * | Ketogenic diet 1.5: 1 * desserts | 4–5 meals (interval 3.5 h) last meal at 23:00 in a ratio of 4: 1 | 1700 kcal * | 148 g (35%) * | 63.7 g (15%) * | 94.4 g (50%) * | Ketocal 4: 1 for a night meal | Tired of the diet |
| 2019/06 | Diet therapy | Ketogenic diet 2.5: 1 | 6 meals (interval 3.5 h) last meal at 23:00 in a ratio of 4: 1 | 2000 kcal | 10.0 g (2%) | 60.0 g (12%) | 190.0 g (86%) | Ketocal 4: 1 for night meal |
⁎
Does not reflect the real situation (elevated TG, fallen ketone bodies)