Table 1.

Statistical comparison of measures of oxidative phosphorylation across fibroblast cell lines.

Parameter	FIB_WT (pmol/min/mg/mL)	FIB_545del (pmol/min/mg/mL)	FIB_65fs (pmol/min/mg/mL)	Significance FIB_WT vs. FIB_545del	Significance FIB_WT vs. FIB_65fs
Non-mitochondrial respiration	27.4 ± 3.059	27.3 ± 1.049	17.42 ± 2.818	ns	p < 0.01
Basal respiration	47.87 ± 4.727	50.15 ± 2.969	39.22 ± 6.709	ns	Ns
Maximal respiration	192.3 ± 43.68	205.9 ± 40.71	96.83 ± 23.8	ns	p < 0.05
ATP production	42.27 ± 4.723	36.3 ± 7.208	30.62 ± 1.91	ns	p < 0.05
Spare respiratory capacity	144.4 ± 44.41	155.7 ± 40.04	57.61 ± 17.59	ns	p < 0.05