FIG. 1.

Ultrastructure of hepatocytes and Kupffer cells of a liver biopsy of CDG‐P1. (A‐B) Hepatocytes showing dilated Golgi (g), autolysosomes (a), multivesicular bodies (MVB), lipolysosomes (LP) with incorporated bubbles containing fibro‐granular material in the bile canalicular zone (bc) and lipid droplets (LD). (C,D) Kupffer cells with lysosomes (L) or multivesicular bodies (MVB) containing dense deposits.