Table 1.

Diagnostic criteria for Kawasaki disease

Criteria	Clinical features
1. Mucosal changes	Erythema and cracking of lips “Strawberry tongue” erythema and prominent fungiform papillae and/or erythema of the oral and pharyngeal mucosa.
2. Conjunctivitis	Bilateral bulbar nonexudative conjunctival injection, often limbic sparing
3. Polymorphous rash	Maculopapular diffuse erythroderma or erythema multiforme-like. Less commonly, urticarial or fine micro-pustular eruptions
4. Extremity changes	Acute phase: erythema and edema of the hands and feet Subacute phase: periungual desquamation
5. Lymphadenopathy	Acute, non-suppurative, cervical lymphadenopathy (≥ 1.5 cm diameter), typically unilateral

To be diagnosed with classic KD, the patient must have ≥ 5 days of fever as well as ≥ 4 of the 5 principal clinical features. In rare cases, experienced clinicians may be able to establish the diagnosis with less than the required duration of fever