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. 2020 Sep 2;11:594. doi: 10.3389/fendo.2020.00594

Table 3.

Differential diagnosis of Stiff-person syndrome.

Differential diagnosis driven by GAD autoantibody positivity
✓ Cerebellar ataxia
✓ Epilepsy
✓ Myoclonus
✓ Neuromyotonia
✓ Batten's disease
✓ Limbic encephalopathy
✓ Myasthenia gravis
Differential diagnosis driven by clinical features
✓Myelopathy
✓ Tetanus
✓ Neuromyotonia
✓ Parkinsonism
✓ Primary lateral sclerosis
✓ Ankylosing spondylitis
✓ Leukodystrophies
✓ Neuroleptic malignant syndrome

GAD, glutamic acid decarboxylase.