Table 2. Pulmonary function test results.
FVC: forced vital capacity; FEV1: forced expiratory volume in one second; TLC: total lung capacity; DLCO: carbon monoxide diffusing capacity.
| Time Frame | FVC/% | FEV1/% | Ratio | TLC | DLCO/% predicted |
| 3 months after presentation | 2.76/98 | 2.23/105 | 81 | 4.36 | 8.6/38 |
| 9 months after presentation | 2.93/107 | 2.23/108 | 76 | 3.60 | 10.0/50 |
| 14 months after presentation | 3.01/111 | 2.40/117 | 80 | 4.61 | 11.1/51 |