Table 1.
Patient baseline characteristics.
Overall (n = 33) | |
---|---|
Gender | |
Male | 24 (72.7%) |
Female | 9 (27.3%) |
Birthweight (kg) | |
Mean (SD) | 3.29 (0.93) |
Median [Min, Max] | 3.34 [1.57, 5.40] |
Missing | 2 (6.1%) |
Age at diagnosis (days) | |
Mean (SD) | 22.8 (74.3) |
Median [Min, Max] | 1 [1, 366] |
Convulsions | |
No | 27 (81.8%) |
Yes | 6 (18.2%) |
Mutation status | |
No mutation | 23 (69.7%) |
Any mutation | 10 (30.3%) |
Glucose at diagnosis (mmol/L) | |
Mean (SD) | 1.39 (0.82) |
Median [Min, Max] | 1.35 [0.10, 4.50] |
Missing | 1 (3.0%) |
Insulin concentration at diagnosis (pmol/L) | |
Mean (SD) | 17.8 (15.9) |
Median [Min, Max] | 12.8 [2.1, 61.1] |
Missing | 4 (12.1%) |
Glucagon dose at stabilization (μg/kg/h) | |
Mean (SD) | 12.4 (5.9) |
Median [Min, Max] | 12.0 [5.0, 20.0] |
Duration of glucagon use (days) | |
Mean (SD) | 33.5 (50.1) |
Median [Min, Max] | 11 [2, 205] |
Missing | 14 (42.4%) |
Diazoxide dose (mg/kg/day) | |
Mean (SD) | 8.97 (4.54) |
Median [Min, Max] | 7.00 [4.00, 15.00] |
Any Octreotide dose | |
No | 22 (66.7%) |
Yes | 11 (33.3%) |