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. 2020 Jul 2;48(16):e91. doi: 10.1093/nar/gkaa550

Table 2.

Genes implicated in mammalian hcoErosions that harbor monogenic disease variants in human patients (disease mutations in HGMD (28))

Gene Associated human monogenic disease Species with gene hcoErosion
A2ML1 • Noonan syndrome Naked mole-rat, brush-tailed rat, guinea pig, chinchilla
• Otitis media (susceptibility to)
CETP • Higher/Lower HDL cholesterol level (I)Bactrian camel, alpaca
• Hyperalphalipoproteinaemia (II)Goat, sheep, Tibetan antelope, cow
• Cholesterol ester transfer protein deficiency
CRYBB3 • Cataract Microbat, big brown bat, David‘s myotis bat
CRYGB • Congenital cataract Cape golden mole, tenrec
EYS • Retinitis pigmentosa Mouse, rat, Chinese hamster, golden hamster, prairie vole
• Retinal dystrophy
• Peripheral dystrophy
• Usher syndrome
FCN2 • FCN2 deficiency Goat, sheep, Tibetan antelope, cow
GCKR • Elevated HDL-cholesterol Microbat, big brown bat, David‘s myotis bat
• Hypertriglyceridaemia
HMGCS2 • Mitochondrial HMG-CoA synthase deficiency Black flying-fox, megabat
HSD3B2 • 3 beta-hydroxysteroid dehydrogenase deficiency Goat, sheep, Tibetan antelope, cow
• Adrenal hyperplasia
• Hypospadias, non-syndromic
• Idiopathic hypospadias
• Pseudohermaphroditism
KLKB1 • Prekallikrein deficiency Dolphin, killer whale
KRT3 • Corneal dystrophy, Meesmann Mouse, rat
MESP1 • Tetralogy of Fallot Naked mole-rat, brush-tailed rat, guinea pig, chinchilla
• Ventricular septal defect
MMP21 • Heterotaxy Pig, dolphin, killer whale, Bactrian camel, alpaca, goat, sheep, Tibetan antelope, cow
MYD88 • MYD88 deficiency Brush-tailed rat, chinchilla
OPTC • Glaucoma, primary open angle Cape golden mole, tenrec, microbat, big brown bat, David‘s myotis bat
PCSK9 • Hypercholesterolaemia (I)Cat, dog, ferret, panda, pacific walrus, Weddell seal
• Low/High LDL cholesterol (II)Goat, sheep, Tibetan antelope, cow
PLA2G2A • Colorectal cancer Dolphin, killer whale
RIPPLY1 • Intellectual disability Black flying-fox, megabat
SFXN4 • Colorectal cancer (I)Chinese hamster, golden hamster, prairie vole
• Mitochondriopathy and macrocytic anaemia (II)Naked mole-rat, brush-tailed rat, guinea pig, chinchilla
STAP1 • Hypercholesterolaemia Dolphin, killer whale
TCN1 • Transcobalamin I deficiency Mouse, rat
TNFRSF6B • Systemic lupus erythematosus Mouse, rat, Chinese hamster, golden hamster, prairie vole
UMOD • Chronic kidney disease Microbat, big brown bat, David‘s myotis bat, black flying-fox, megabat
• Congenital anomalies of the kidney and urinary tract
• FJHN/MCKD syndrome
• Glomerulocystic kidney disease
• Uromodulin-associated kidney disease
• Hyperuricaemic nephropathy
XAF1 • Multiple sessile serrated adenoma Cat, dog, ferret, panda, pacific walrus, Weddell seal
ZNF543 • IgA nephropathy Cat, dog, ferret, panda, pacific walrus, Weddell seal
ZNF589 • Intellectual disability Ferret, panda, pacific walrus, Weddell seal
ZP1 • Infertility Pig, dolphin, killer whale, Bactrian camel, alpaca, goat, sheep, Tibetan antelope, cow

(I), (II) Independent hcoErosion loss events: (I) species belonging to group I (II) species belonging to group II.