Table 1:

Hamburg and Weill Cornell scales for assessing functional ability in patients with neuronal ceroid lipofuscinosis type 2 disease

	Hamburg scale		Weill Cornell scale
	Motor	Language	Gait	Language
Score 3	Walks normally	Normal	Normal	Normal
Score 2	Frequent falls, obvious clumsiness	Recognisably abnormal	Abnormal but independent	Abnormal
Score 1	No unaided walking or crawling only	Hardly understandable	Abnormal, requires assistance	Barely understandable
Score 0	Immobile, mostly bedridden	Unintelligible or no language	Non-ambulatory	Unintelligible or no speech

Adapted from Steinfeld et al¹⁷ and Worgall et al.¹⁸