Table 2.
The result of examination on patients in the conference
| Total participants (n = 22) | |
|---|---|
| Participant sex (M:F) | 10:12 |
| Age at onset (n = 19)a | 43.4 ± 8.9 |
| Age at diagnosis (n = 17)a | 49 ± 7.9 |
| Age at participationa | 55.2 ± 9.9 |
| Forced vital capacity, % predictedb (range) | 82 ± 25 (48–146) |
| ALS-CBSb,c (range) | 17.1 ± 1.6 (14–20) |
| Facial weakness | 11 (50%) |
| Weakness of eye closure | 7 (32%) |
| Weakness of lip closure | 9 (41%) |
| Scapular winging | 12 (55%) |
| Bilateral | 5 (23%) |
| Unilateral | 7 (32%) |
| IBM-FRSb,d (range) | 29.0 ± 7.0 (9–39) |
| Timed up and go testb,e (n = 17, s, range) | 12.2 ± 6.0 (5.0–27.6) |
| Walking aid | 14 (64%) |
| Cane | 9 (41%)f |
| Walker | 11(50%)g |
| Wheelchair | 5 (23%)h |
a,bMean ± SD, years
cAmyotrophic Lateral Sclerosis Cognitive Behavioral Screen (ALS-CBS) is a screening tool for frontal lobe dysfunction. We used the cognitive section of ALS-CBS whose total score is 20
dInclusion Body Myositis Functional Rating Scale (IBM-FRS) consists of 10 questions about a patient’s ability to perform daily activities, such as walking, dressing, and handling utensils. Each question was answered using a number 0–4
eThe Timed Up and Go test is a test for quantifying functional mobility and assessing the fall risk, in which the ability to rise from a seated chair position, walk 3 m, turn, walk back, and sit down is timed
fAmong the nine patients, five patients always used a cane, while four patients only sometimes used it
gAmong the eleven patients, two patients always used a walker, while nine patients only sometimes used it
hAmong the five patients, one patient always used a wheelchair, while four patients only sometimes used it