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. Author manuscript; available in PMC: 2022 Jan 1.
Published in final edited form as: J Vasc Surg. 2020 Apr 8;73(1):161–171. doi: 10.1016/j.jvs.2020.02.046

Table 3. Segmental Renal Artery Specimens: 2 in 2 Children.

[M-male, F-female; c-concentric, e-eccentric; min-minimal, mod-moderate, extn-extensive; IF-intimal fibrodysplasia (cellular accumulations), IEL-internal elastic lamina, dupl-duplication, disrp-disrupted; sctM-scant media, discnM-discontinuous media, MF-media fibrodysplasia (disorganized smooth muscle, increased ground substances); AF-adventitial fibrodysplasia (increased cellular and ground substances); Ao-aorta, AbdAoCoarc-abnormal aortic coarctation; SMA=-superior mesenteric artery, CA-celiac artery; NF-1-neurofibromatosis-1, NoDA-no distinct abnormality]

Age (yr) Sex Intima Media Adventitia Dominant Abnormality Comment
1 4M cIF(extn), luminal thrombus NoDA AF(extn) IF, AF ---
2 7F NoDA NoDA AF(extn) AF AbdAoCoarc (suprarenal), NF-1