Table 3. Segmental Renal Artery Specimens: 2 in 2 Children.
[M-male, F-female; c-concentric, e-eccentric; min-minimal, mod-moderate, extn-extensive; IF-intimal fibrodysplasia (cellular accumulations), IEL-internal elastic lamina, dupl-duplication, disrp-disrupted; sctM-scant media, discnM-discontinuous media, MF-media fibrodysplasia (disorganized smooth muscle, increased ground substances); AF-adventitial fibrodysplasia (increased cellular and ground substances); Ao-aorta, AbdAoCoarc-abnormal aortic coarctation; SMA=-superior mesenteric artery, CA-celiac artery; NF-1-neurofibromatosis-1, NoDA-no distinct abnormality]
| Age (yr) Sex | Intima | Media | Adventitia | Dominant Abnormality | Comment | |
|---|---|---|---|---|---|---|
| 1 | 4M | cIF(extn), luminal thrombus | NoDA | AF(extn) | IF, AF | --- |
| 2 | 7F | NoDA | NoDA | AF(extn) | AF | AbdAoCoarc (suprarenal), NF-1 |