Table 2. Distributions of patients with congenital coagulation disorders according to region for 6 years.
| Region | HA | HB | vWD | Factor XI def. | Others | Total | % |
|---|---|---|---|---|---|---|---|
| Gyeonggi | 166 (2.23) | 35 (0.46) | 101 (1.35) | 30 (0.39) | 117 (1.55) | 449 | 22.1 |
| Seoul | 139 (2.37) | 20 (0.34) | 99 (1.67) | 26 (0.43) | 105 (1.82) | 389 | 19.2 |
| Gyeongnam | 58 (2.83) | 9 (0.45) | 23 (1.13) | 4 (0.19) | 78 (3.84) | 172 | 8.5 |
| Gyeongbuk | 36 (2.34) | 6 (0.36) | 52 (3.51) | 5 (0.34) | 35 (2.23) | 134 | 6.6 |
| Daegu | 36 (2.50) | 6 (0.40) | 70 (4.78) | 3 (0.19) | 18 (1.25) | 133 | 6.6 |
| Busan | 47 (2.29) | 9 (0.47) | 24 (1.28) | 3 (0.15) | 38 (1.92) | 121 | 6.0 |
| Daejeon | 56 (5.81) | 7 (0.73) | 11 (1.16) | 3 (0.31) | 10 (1.07) | 87 | 4.3 |
| Chungnam | 39 (3.16) | 5 (0.42) | 13 (1.05) | 1 (0.07) | 20 (1.61) | 78 | 3.8 |
| Incheon | 36 (2.08) | 10 (0.59) | 12 (0.70) | 6 (0.34) | 13 (0.78) | 77 | 3.8 |
| Jeonnam | 33 (3.05) | 6 (0.49) | 22 (2.07) | 4 (0.37) | 6 (0.49) | 71 | 3.5 |
| Jeonbuk | 27 (2.46) | 3 (0.30) | 20 (1.78) | 1 (0.08) | 14 (1.25) | 65 | 3.2 |
| Gwangju | 24 (2.61) | 5 (0.54) | 25 (2.73) | 1 (0.12) | 8 (0.88) | 63 | 3.1 |
| Gangwon | 25 (2.78) | 1 (0.11) | 14 (1.65) | 2 (0.23) | 15 (1.69) | 57 | 2.8 |
| Chungbuk | 11 (1.19) | 5 (0.49) | 14 (1.51) | 1 (0.10) | 20 (2.14) | 51 | 2.5 |
| Ulsan | 13 (1.93) | 1 (0.14) | 6 (0.82) | 0 (0) | 8 (1.19) | 28 | 1.4 |
| Jeju | 9 (2.35) | 1 (0.25) | 6 (1.82) | 1 (0.23) | 5 (1.48) | 22 | 1.1 |
| Sejong | 3 (3.36) | 0 (0) | 2 (2.17) | 0 (0) | 0 (0) | 5 | 0.2 |
| Missing data | 17 | 3 | 3 | 1 | 3 | 27 | 1.3 |
| Total | 775 | 132 | 517 | 92 | 513 | 2,029 | 100.0 |
Values are expressed as number (age standardized incidence rate).
HA = hemophilia A, HB = hemophilia B, vWD = von Willebrand disease.