Official websites use .gov
A
.gov website belongs to an official
government organization in the United States.
Secure .gov websites use HTTPS
A lock (
) or https:// means you've safely
connected to the .gov website. Share sensitive
information only on official, secure websites.
Putative mechanisms responsible for secondary CoQ10 in disease in MPS, PKU and METC disorders. Oxidative stress (OS), pyridoxal 5-phosphate (PLP), mucopolysaccharidosis (MPS), phenylketonuria (PKU), phenylalanine (Phe) and mitochondrial electron transport chain (METC). Black arrows represent defined biochemical reactions; red arrows represent tentative biochemical reactions. ‘X‘ represents the inhibition of an enzyme or biosynthetic step.
