APAH	associated pulmonary arterial hypertension
AVT	acute vasoreactivity testing
ASD	atrial septal defect
AVSD	atrioventricular septal defect
BMPRII	bone morphogenetic protein receptor 2
BNP	brain natriuretic peptide
BPA	balloon pulmonary angioplasty
BPD	Bronchopulmonary dysplasia
CCB	calcium channel blocker
CHD	congenital heart disease
CI	cardiac index
COPD	chronic obstructive pulmonary disease
CTEPH	chronic thromboembolic pulmonary hypertension
DLTX	Double lung transplantation
DPG	diastolic pressure gradient (diastolic PAP—mean PAWP)
ECMO	extracorporeal membrane oxygenation
ES	Eisenmenger Syndrome
ERA	endothelin receptor antagonist
FC	functional class
HPAH	heritable pulmonary arterial hypertension
HLHS	hypoplastic left heart syndrome
HLTX	Heart lung transplantation
HFrEF	heart failure with reduced ejection fraction
IPAH	idiopathic pulmonary arterial hypertension
LH	left heart disease
LV	left ventricle/ventricular
LVEDP	left ventricular end-diastolic pressure
MAPCAS	major aorto-pulmonary collateral arteries
MCS	mechanical circulatory support
NO	nitric oxide
NT-proBNP	N-terminal pro-brain natriuretic peptide
PPAT	Pulmonary artery acceleration time
PAH	pulmonary arterial hypertension
PAP	pulmonary arterial pressure
PAPm	mean pulmonary arterial pressure
PAPs	systolic pulmonary arterial pressure
PAWP	pulmonary artery wedge pressure
PHVD	Pulmonary hypertensive vascular disease
PDA	persistent ductus arteriosus
PDE-5i	phosphodiesterase type 5 inhibitor
PPHN	persistent pulmonary hypertension of the new-born
PLE	pleural effusion
PVR	pulmonary vascular resistance
6MWD/6MWT	6-min walking distance/6-min walking test
RAP	Right atrial pressure
SCD	sickle cell disease
S/D ratio	systolic to diastolic duration ratio
SVR	systemic vascular resistance
T21	Trisomy 21 or Down Syndrome
TPG	transpulmonary gradient (mean PAP- mean PAWP)
TAC	Truncus arteriosus communis
TRV	tricuspid regurgitation velocity
VAD	ventricular assist device
VSD	ventricular septal defect
WHO-FC	World Health Organization functional class
WU	Wood Units
WSPH	World Symposium on Pulmonary hypertension