Figure 2.

Kidney biopsy with electron microscopy with typical lamelar inclusions in a 27-year old Fabry male patient with normal kidney function (eGFR 102 mL/min/1.73 m²), normoalbuminuria (ACR 12 mg/g), but high levels of podocyturia (UPod 2.420/g creatinine). Diffuse and numerous myeloid inclusions in podocyte cytoplasm (black arrow) with presence of vacuoles in the cytoplasm of podocytes (white arrow) are evident. Figure courtesy of Pleško J and Kojc N; Institute of Pathology, Ljubljana Medical Faculty.