Table 2.
Full-Field Electroretinogram Findings of Patients Diagnosed With Mitochondrial Disease
| Patient ID | Scotopic Response OD/OS, µV | Scotopic Response Implicit Time OD/OS, ms | Maximum Response OD/OS A Wave, µV | Maximum Response OD/OS B Wave, µV | Cone Response OD/OS A Wave, µV | Cone Response OD/OS B Wave, µV | 30 Hz Flicker OD/OS, µV | 30 Hz Flicker Implicit Time OD/OS, ms |
|---|---|---|---|---|---|---|---|---|
| P1 | Extinguished | Extinguished | Extinguished | Extinguished | Extinguished | Extinguished | 6.5/7.3 | 39/39 |
| P2 | NA | NA | NA | NA | NA | NA | NA | NA |
| P3 | 98.2/119.2 | 76/94 | −70.9/−83.4 | 168.7/167.1 | −25.2/−16.4 | 108.5/72.4 | 45.5/36.7 | 30/28 |
| P4 | 120.7/219.2 | 73/74 | −143.5/−238.1 | 201/383 | −26.7/−23.9 | 90.7/126.1 | 37.1/75.4 | 28/28 |
| P5 | 181.1/230.8 | 52/52 | −111.1/−117.5 | 171.6/231.5 | −32.4/−19.3 | 74.6/102.7 | 28/50 | 37/37 |
| P6 | Extinguished | Extinguished | Extinguished | Extinguished | Extinguished | Extinguished | 1.1/0.4 | 37/36 |
| P7 | 260.5/212.8 | 96/98 | −149.9/−140.6 | 254.4/270.4 | −13.0/−17.4 | 64.0/34.5 | 43.8/46.9 | 26/31 |
| P8 | 83.7/52.6 | 83/87 | −89.1/−60.6 | 146.6/102.8 | −4.4/−5.4 | 51.0/29.9 | 34.1/29.1 | 28/30 |
| P9 | 130.5/222.6 | 107/89 | −210.8/−266.1 | 342/404.4 | −36.3/−27.7 | 105.4/134.8 | 70.1/98.6 | 32/27 |
| Normal | 218.5 ± 148.3 | 85.9 ± 14.1 | −210.1 ± 172.1 | 347.0 ± 134.1 | −36.4 ± 25.8 | 109.8 ± 67.8 | 121.4 ± 65.5 | 26.3 ± 3.8 |
OD, right eye; OS, left eye; NA, not available.