. Author manuscript; available in PMC: 2020 Oct 23.

Published in final edited form as: Histopathology. 2017 Dec 4;72(4):588–600. doi: 10.1111/his.13395

Table 1:

Fumarate Hydratase Deficient RCC

Case	Age/Sex	Size/Stage	Notable pathologic features	Clinical history
FH #1	25/M	Multifocal. 4 nodules (4–62mm) pT1Nx	Nested, solid and cystic, oncocytoma-like	No f/u available
FH #2	10/F	5.5 cm, extensively cystic grossly pT1N0Mx	Nested tubular and cystic	Presented with hypertension No h/o neoplasia or genetic syndrome NED x 24 months
FH #3	19/F	3.0 cm pT1Nx (partial nephrectomy)	Nested tubular; originally diagnosed as oncocytoma	No f/u available
FH #4	17/F	16cm pT3aNX	Nested tubular	No f/u available

f/u= follow-up; h/o= history of; NED= no evidence of disease