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. 2020 Apr 22;145(7):413–420. doi: 10.1159/000507075

Table 1.

Clinical baseline characteristics

Total group (n = 20)
Age, years 39±12
Gender, male 11 (55)
Family history of SCD in first-degree relatives 8 (40)
History of atrial flutter at age <35 years 1 (5)
Symptoms
 Palpitations 11 (55)
 Syncope 9 (45)
 Near syncope 4 (20)
Systemic systolic ventricular function
 Normal left ventricular ejection fraction (≥55%) 20 (100)
Genetic variance
 No (likely) pathogenic SCN5A variant 14 (70)
 No genetic testing 4 (20)
 Pathogenic SCN5A variant 2 (10)
Clinical presentation
 Ajmaline induced Brugada ECG 14 (70)
 Fever induced Brugada ECG 4 (20)
 Spontaneous Brugada ECG 2 (10)

Electrocardiography
 Sinus rhythm 20 (100)
 PR interval, ms 169±28
 QRS duration, ms 103±18
 QTc duration, ms 391±22
 Fragmented QRS 4 (20)
EP study 7 (35)
 No inducible sustained VA 7 (35)
 VERP <200 ms 2 (10)
Holter monitoring 16 (80)
 No PVCs 10 (50)
 ≤1% PVCs 6 (30)
 Supraventricular tachycardia 0
 Ventricular tachycardia 0
SA-ECG 16 (80)
 Late potentials 10 (50)

Data are presented as n (%) or mean ± standard deviation. ECG, electrocardiogram; EP, electrophysiological; PVC, premature ventricular arrhythmia; SCD, sudden cardiac death; VA, ventricular arrhythmia; VERP, ventricular effective refractory period.